Table 1 WHO classification of soft tissue tumours (2013) including for the first time nerve sheath tumours [12]

Benign

Malignant

Schwannoma (including variants)

Malignant peripheral nerve sheath tumour

Melanotic schwannoma

Epithelioid malignant nerve sheath tumour

Neurofibroma (including variants)

Malignant Triton tumour

 Plexiform neurofibroma

Malignant granular cell tumour Ectomesenchymoma

Perineurioma

 Malignant perineurioma

Granular cell tumour

Dermal nerve sheath myxoma

Solitary circumscribed neuroma

Ectopic meningioma

Nasal glial heterotopia

Benign Triton tumour

Hybrid nerve sheath tumours