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Table 1 Classification of malignant primary bone tumours (adapted from WHO classification [14])

From: UK guidelines for the management of bone sarcomas

Chondrogenic tumours

(1) Atypical cartilaginous tumour/chondrosarcoma (grade I)

(2) Chondrosarcoma (grades II/III)

(3) Dedifferentiated chondrosarcoma

(4) Mesenchymal chondrosarcoma

(5) Clear cell chondrosarcoma

Osteogenic tumours

(1) Low-grade central osteosarcoma

(2) Conventional (high-grade) osteosarcoma (chondroblastic fibroblastic osteoblastic)

(3) Telangiectatic osteosarcoma

(4) Small cell osteosarcoma

(5) Secondary osteosarcoma

(6) Parosteal osteosarcoma

(7) Periosteal osteosarcoma

(8) High-grade surface osteosarcoma

Notochordal tumours

Chordoma

Vascular tumours

(1) Epithelioid haemangioendothelioma

(2) Angiosarcoma

Other malignant mesenchymal tumours

Fibrosarcoma, Leiomyosarcoma, Liposarcoma etc.

Miscellaneous tumours

(1) Ewing sarcoma

(2) Adamantinoma

(3) Undifferentiated high-grade pleomorphic sarcoma of bone