Total (n = 9) | |
---|---|
Sex | |
Male | 8 |
Female | 1 |
Age at histological diagnosis (years) | |
Mean (SD) | 27,3 |
Range (years) | 9–48 |
Tumor localization | |
Abdomen | 7 |
Head and neck | 1 |
Pelvis | 1 |
Histological subtype | |
DSRCT | 4 |
Desmoplastic medulloblastoma | 1 |
Desmoplastic tumor with multiple differentiation | 2 |
Unclassified desmoplastic tumor | 2 |
Tumor stage (AJCC/IUCC) | |
Unknown | 2 |
IVB | 7 |
Metastases at diagnosis | |
Yes | 6 |
Liver | 4 |
Peritoneum | 2 |
Other | 1 |
Surgery of primary tumor | |
Yes | 7 |
Resection quality | |
R0 | 0 |
R1 | 3 |
R2 | 2 |
Unknown | 2 |