From: Non-canonical WNT6/WNT10A signal factor expression in EBV+ post-transplant smooth muscle tumors
Entities | PTSMT | Leiomyoma (LM) | Leiomyosarcoma (LMS) | Angioleiomyoma (ALM) | Endothelial haemangioma (EHA) |
---|---|---|---|---|---|
Number of tumors | n = 6 (5 patients) | n = 9 | n = 4 | n = 28 | n = 5 |
Age (median, range) | 11.5 (6–61) | 60 (29–71) | 63 (45–71) | 60 (23–79) | 48 (32–58) |
Gender | ♀ 100% ♂ 0% | ♀ 89% ♂ 11% | ♀ 75% ♂ 25% | ♀ 64% ♂ 36% | ♀ 60% ♂ 40% |
Tumor localisation | Kidney (n = 2) Lung (n = 1) Colon (n = 1) Spleen (n = 1) Confluens sinuum (n = 1) | Stomach (n = 3) Kidney (n = 2) Skin (n = 2) Esophagus (n = 1) Mesenterium (n = 1) | Pulmonary artery (n = 2) Right atrium (n = 1) Adrenal gland vein (n = 1) | Lower extremities (n = 13) Upper extremities (n = 2) Head–Neck (n = 3) Genital ♀ (n = 2) Skin/soft tissue (n = 8) | Lower extremities (n = 3) Head–Neck (n = 1) Mediastinal (n = 1) |