TY - JOUR AU - Paoluzzi, Luca AU - Ghesani, Munir PY - 2018 DA - 2018/12/05 TI - Extraskeletal myxoid chondrosarcoma with massive pulmonary metastases JO - Clinical Sarcoma Research SP - 20 VL - 8 IS - 1 AB - Extraskeletal myxoid chondrosarcoma (EMC) is a rare malignant mesenchymal neoplasm of uncertain differentiation characterized by rearrangements of the NR4A3 gene. EMC often affects adults around the age of 50 and arise in the deep tissues of the proximal extremities and limb girdles. EMC is characterized by indolent growth rate but strong tendency to local recurrence and metastatic spread. No systemic treatment is specifically approved by the FDA for this disease and surgery has been traditionally the only potentially curative strategy. SN - 2045-3329 UR - https://doi.org/10.1186/s13569-018-0108-8 DO - 10.1186/s13569-018-0108-8 ID - Paoluzzi2018 ER -