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Table 1 Bohan and Peter’s proposed diagnostic criteria for dermatomyositis

From: Paraneoplastic dermatomyositis associated with metastatic leiomyosarcoma of unknown primary

Criterion
I Symmetrical proximal muscle weakness ± dysphagia or respiratory muscle involvement
II Increase of skeletal muscle enzymes; creatine kinase, aspartate aminotransferase, alanine aminotransferase and lactate dehydrogenase
III Abnormal EMG characteristic of myopathy
IV Abnormal muscle biopsy
V Typical cutaneous features (e.g. Gottron’s sign, heliotrope rash with periorbital oedema)
Definite diagnosis: Criterion V and at least 3 of criteria I–IV
Probable diagnosis: Criterion V and 2 of criteria I–IV
Possible diagnosis: Criterion V and 1 of criteria I–IV