From: Simultaneous diagnosis of liver PEComa in a family with known Li–Fraumeni syndrome: a case report
Prognosis | Risk factors |
---|---|
Benign | < 2 risk factors Size < 5 cm |
Uncertain malignant potential | Size > 5 cm with no other risk criteria or only cell pleomorphism/multi-nuclear giant cells |
Malignant | 2 or more risk factors |