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Table 2 PEComa prognostic classification

From: Simultaneous diagnosis of liver PEComa in a family with known Li–Fraumeni syndrome: a case report

Prognosis

Risk factors

Benign

< 2 risk factors

Size < 5 cm

Uncertain malignant potential

Size > 5 cm with no other risk criteria or only cell pleomorphism/multi-nuclear giant cells

Malignant

2 or more risk factors